Hepatoid Carcinoma

Hepatoid carcinoma is a rare and aggressive malignancy that occurs when abnormal hepatoid/liver cells are found outside of the liver. These tumours resemble hepatocellular carcinoma (HCC), which is one of the most common types of liver cancer. 

Hepatoid carcinomas are most commonly found in the stomach, however they have also been found in the pancreas, ovaries, lungs, gallbladder, uterus, bladder and/or ampulla of Vater (a small opening where the bile and pancreatic ducts empty into the small intestine).  

Hepatoid carcinomas are more common in men, and is often diagnosed around the age of 55. However, anyone can develop this disease. 

Treatment

If a hepatoid carcinoma is detected, it will be staged and graded based on size, metastasis, and how the cancer cells look under the microscope. Staging and grading helps your doctors determine the best treatment for you.  

Cancers can be staged using the TNM staging system:  

  • T (tumour) indicates the size and depth of the tumour.  
  • N (node) indicates whether the cancer has spread to nearby lymph nodes.  
  • M (metastasis) indicates whether the cancer has spread to other parts of the body.  

This system can also be used in combination with a numerical value, from stage 0-IV:  

  • Stage 0: this stage describes cancer cells in the place of origin (or ‘in situ’) that have not spread to nearby tissue.  
  • Stage I: cancer cells have begun to spread to nearby tissue. It is not deeply embedded into nearby tissue and had not spread to lymph nodes. This stage is also known as early-stage cancer.  
  • Stage II: cancer cells have grown deeper into nearby tissue. Lymph nodes may or may not be affected. This is also known as localised cancer.  
  • Stage III: the cancer has become larger and has grown deeper into nearby tissue. Lymph nodes are generally affected at this stage. This is also known as localised cancer.  
  • Stage IV: the cancer has spread to other tissues and organs in the body. This is also known as advanced or metastatic cancer.  

Cancers can also be graded based on the rate of growth and how likely they are to spread:  

  • Grade I: cancer cells present as slightly abnormal and are usually slow growing. This is also known as a low-grade tumour.  
  • Grade II: cancer cells present as abnormal and grow faster than grade-I tumours. This is also known as an intermediate-grade tumour.   
  • Grade III: cancer cells present as very abnormal and grow quickly. This is also known as a high-grade tumour.   

Once your tumour has been staged and graded, your doctor may recommend genetic testing, which analyses your tumour DNA and can help determine which treatment has the greatest chance of success. They will then discuss the most appropriate treatment option for you.   

Treatment is dependent on several factors, including location, age, stage of disease and overall health.  

Treatment options for hepatoid carcinoma may include:  

  • Surgery to remove as much of the tumour(s) as possible – varies based on tumour location(s). 
  • Radiation therapy. 
  • Chemotherapy (may not be recommended for all patients). 
  • Clinical trials. 
  • Palliative care. 

Risk factors

Because of how rare hepatoid carcinomas are, there has been limited research done into the risk factors of this disease.  

Symptoms

Hepatoid carcinomas may appear asymptomatic in the early stages of disease. As the tumour progresses, some of the following symptoms may appear: 

  • Abdominal pain, discomfort and/or swelling.  
  • Fatigue. 
  • Unexplained weight loss/loss of appetite. 
  • Nausea and/or vomiting. 
  • Elevated alpha fetoprotein (AFP). 

Not everyone with the symptoms above will have cancer, but see your general practitioner (GP) if you are concerned. 

Diagnosis

If your doctor suspects you have hepatoid carcinoma, they may order the following tests to confirm the diagnosis and refer you to a specialist for treatment.:

  • Physical examination.
  • Imaging tests, potentially including:
    • MRI (magnetic resonance imaging).
    • CT (computed tomography) scan.
  • Blood tests.
  • Exploratory surgery.
  • Biopsy.

References

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